3-Hydroxyisovalerylcarnitine

Name: 3-Hydroxyisovalerylcarnitine | 99159-87-2
Brand: US-CATO
SKU: S57C1929872_1_MG
Price: 19998.0 USD
Availability: OutOfStock

Cat. No S57C1929872_1_MG

Vendor: US-CATO

Product Information

Product Name

3-Hydroxyisovalerylcarnitine

Brand Name

US-CATO

Product Number

C1929872

CAS

99159-87-2

Certificate of Analysis (COA)

COA not found

General Information

PubChem CID

131668011

IUPAC Name

(3R)-3-(3-hydroxy-3-methylbutanoyl)oxy-4-(trimethylazaniumyl)butanoate

InChI Key

IGLHHSKNBDXCEY-SECBINFHSA-N

SMILES

CC(C)(CC(=O)OC@H(CC(=O)O-)CN+(C)(C)C)O

References Data Source From Pubchem

A metabolome atlas of the aging mouse brain.

Publication Name: Nature Communications

Publication Date: 2021-10-15

DOI: 10.1038/s41467-021-26310-y

3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: Clinical presentation and outcome in a series of 37 patients

Publication Name: Molecular Genetics and Metabolism

Publication Date: 2017-07

DOI: 10.1016/j.ymgme.2017.05.014

[Determination of 3-hydroxyisovaleryl carnitine in plasma and urinary excretion by ultra-performance liquid chromatography-tandem mass spectrometry]

Publication Name: Wei sheng yan jiu = Journal of hygiene research

Publication Date: 2016-05

Increased oxidative stress in patients with 3-hydroxy-3-methylglutaric aciduria

Publication Name: Molecular and Cellular Biochemistry

Publication Date: 2015-01-04

DOI: 10.1007/s11010-014-2322-x

Is L-Carnitine Supplementation Beneficial in 3-Methylcrotonyl-CoA Carboxylase Deficiency?

Publication Name: JIMD reports

Publication Date: 2015

DOI: 10.1007/8904_2014_393

3-Hydroxyisovalerylcarnitine

Product Information

General Information

References Data Source From Pubchem

A metabolome atlas of the aging mouse brain.

3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: Clinical presentation and outcome in a series of 37 patients

[Determination of 3-hydroxyisovaleryl carnitine in plasma and urinary excretion by ultra-performance liquid chromatography-tandem mass spectrometry]

Increased oxidative stress in patients with 3-hydroxy-3-methylglutaric aciduria

Is L-Carnitine Supplementation Beneficial in 3-Methylcrotonyl-CoA Carboxylase Deficiency?